Behet's Syndrome From Pathogenesis to Treatment [Paperback]

Beh?et's syndrome can reasonably be considered a unique entity among diseases of the immune system for several reasons: It has specific features and, uniquely among the immune system pathologies, represents a link between autoimmune diseases, systemic vasculitis, and autoinflammatory diseases. In addition, it is of interest to a variety of specialists, including immunologists, rheumatologists, dermatologists, and ophthalmologists, and requires a complex multidisciplinary approach. Many aspects need to be considered in a syndrome that presents a wide spectrum of symptoms and for which the therapeutic armamentarium is expanding significantly, with the development of new treatments, not least the so-called biologics. This book offers comprehensive coverage of the disease by some of the worlds leading experts in Beh?et's syndrome from all the relevant specialties. Epidemiology, genetics, pathogenesis, organ system involvement, differential diagnosis, novel treatments, surgical management, and prognosis are just some of the topics addressed. Beh?et's Syndrome: From Pathogenesis to Treatment will be an invaluable reference for a range of practitioners, researchers, and undergraduates or postgraduates interested in immuno-rheumatology, dermatology, and rare diseases. ? ?This book offers comprehensive coverage by leading experts in Beh?et's syndrome from all relevant specialties. Coverage includes genetics, organ system involvement, differential diagnosis, novel treatments, surgical management, and prognosis.

Preface 1 Beh?et syndrome.- Preface 2 Beh?et's syndrome: the role of patient's Associations.- The numbers of Beh?et: a rare disease.- Along the Old Silk Road.- Epidemiology of Beh?et's syndrome.- Beh?et's syndrome according to classical and population genetics.- Infections, autoimmunity and Beh?ets syndrome: what liaison.- Pathogenesis of Beh?et's syndrome.- Muco-cutaneous involvement in Beh?et's syndrome.- Neurological and neuro-psychological manifestation lS.